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Заболевание встречается редко (1–2 случая на 100 тыс. человек в год), чаще у женщин (соотношение 3:1) [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). Без лечения постепенно прогрессирует и вызывает тяжёлые осложнения [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). При своевременной диагностике и терапии возможна длительная ремиссия [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/).\n\n## Причины\nТочные причины АИГ неизвестны, но выделяют несколько вероятных факторов риска [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/): \n* **Генетическая предрасположенность** — связь с генами HLA (DR3 и DR4), которые регулируют иммунный ответ [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Вирусные инфекции** — запустить развитие аутоиммунного воспаления печени могут вирусы гепатита А, В, С, герпеса, кори, Эпштейна-Барра [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Приём лекарств** — применение средств, влияющих на работу иммунной системы, может быть одной из причин поражения печени [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/).\n\n## Симптомы\nКлинические проявления АИГ разнообразны [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). У одних людей заболевание на протяжении многих лет протекает бессимптомно, у других быстро приводит к печёночной недостаточности [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). Некоторые признаки: \n* общая слабость и быстрая утомляемость [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* тошнота, потеря аппетита [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* боль в правом подреберье [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* желтуха (пожелтение кожи и склер) [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* боли в мышцах и суставах [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/); \n* кожный зуд [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n\nИногда АИГ развивается остро — в этом случае по симптомам напоминает вирусный гепатит: повышается температура тела, появляется выраженная желтуха, в крови отмечают рост печёночных ферментов [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/).\n\n## Диагностика\nДиагностику назначает терапевт, гастроэнтеролог или гепатолог [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). Обследование может включать: \n* **Биохимический анализ крови** — определяют повышение АЛТ, АСТ и билирубина [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Анализы крови на антитела** — выявляют антинуклеарные антитела (ANA), антигладкомышечные антитела (SMA), печёночно-почечные (LKM) и др. [1](https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/). \n* **Инструментальные методы** — ультразвуковое исследование печени, компьютерная томография (КТ) или магнитно-резонансная томография (МРТ) [11](https://shifa-msk.ru/articles/meditsinskiy-tsentr/terapiya/autoimmunnyy-gepatit-simptomy-diagnostika-i-metody-lecheniya/). \n* **Печёночная биопсия** — позволяет оценить степень воспаления и фиброза, а также подтвердить аутоиммунный характер гепатита [11](https://shifa-msk.ru/articles/meditsinskiy-tsentr/terapiya/autoimmunnyy-gepatit-simptomy-diagnostika-i-metody-lecheniya/).\n\n## Лечение\nЛечение АИГ направлено на подавление иммунного ответа, уменьшение воспаления, предотвращение прогрессирования заболевания и защиту печени от дальнейшего повреждения [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). Некоторые методы: \n* **Медикаментозная терапия** — использование кортикостероидов (например, преднизолона) и других иммуносупрессивных препаратов [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). \n* **Поддерживающая терапия** — диета, регулярный мониторинг состояния пациента и уровня печёночных ферментов [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). \n* **Хирургическое вмешательство** — в тяжёлых случаях, когда аутоиммунный гепатит приводит к необратимым изменениям в печени, может потребоваться трансплантация печени [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). \n\nЛечение обычно длительное и может продолжаться в течение многих лет [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/). Регулярный мониторинг состояния пациента и уровня печёночных ферментов необходим для оценки эффективности терапии и предотвращения побочных эффектов [15](https://premium-clinic.ru/metody-lecheniya-autoimmunnogo-gepatita/).","linksData":[{"sourceId":1,"url":"https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/","shownUrl":"https://www.fdoctor.ru/bolezn/autoimmunnyy_gepatit/","title":"Аутоиммунный гепатит - причины, симптомы, методы диагностики и лечения.","shortUrl":"fdoctor.ru","isTranslated":false,"description":"","greenUrl":"fdoctor.ru"},{"sourceId":2,"url":"https://doct.ru/diseases/autoimmunniy-gepatit.html","shownUrl":"https://doct.ru/diseases/autoimmunniy-gepatit.html","title":"Аутоиммунный гепатит - причины, симптомы, диагностика и лечение","shortUrl":"doct.ru","isTranslated":false,"description":"","greenUrl":"doct.ru"},{"sourceId":3,"url":"https://kapmed.ru/spravochnyi-centr/stati-i-instruktsii/autoimmunnyy-gepatit/","shownUrl":"https://kapmed.ru/spravochnyi-centr/stati-i-instruktsii/autoimmunnyy-gepatit/","title":"Аутоиммунный гепатит: симптомы и лечение | Капитал МС","shortUrl":"kapmed.ru","isTranslated":false,"description":"","greenUrl":"kapmed.ru"},{"sourceId":4,"url":"https://www.yamed.ru/services/gepatologiya/autoimmunnyy-gepatit/","shownUrl":"https://www.yamed.ru/services/gepatologiya/autoimmunnyy-gepatit/","title":"Аутоиммунный гепатит — причины появления, симптомы и лечение","shortUrl":"yamed.ru","isTranslated":false,"description":"","greenUrl":"yamed.ru"},{"sourceId":5,"url":"https://klinikarassvet.ru/patients/zabolevanija/autoimmunnyy-gepatit/","shownUrl":"https://klinikarassvet.ru/patients/zabolevanija/autoimmunnyy-gepatit/","title":"Аутоиммунный гепатит: симптомы и лечение | Клиника Рассвет","shortUrl":"klinikarassvet.ru","isTranslated":false,"description":"","greenUrl":"klinikarassvet.ru"},{"sourceId":6,"url":"https://www.invitro.ru/library/chem-boleyut-nashi-deti/57404/","shownUrl":"https://www.invitro.ru/library/chem-boleyut-nashi-deti/57404/","title":"Аутоиммунный гепатит у детей - причины появления, симптомы заболевания, диагностика и способы лечения","shortUrl":"invitro.ru","isTranslated":false,"description":"","greenUrl":"invitro.ru"},{"sourceId":7,"url":"https://comfort.sovamed.ru/zabolevaniya/autoimmunnye-zabolevaniya-pecheni/","shownUrl":"https://comfort.sovamed.ru/zabolevaniya/autoimmunnye-zabolevaniya-pecheni/","title":"Аутоиммунные заболевания печени: причины, симптомы и лечение","shortUrl":"comfort.sovamed.ru","isTranslated":false,"description":"","greenUrl":"comfort.sovamed.ru"},{"sourceId":8,"url":"https://ProBolezny.ru/autoimmunnyy-gepatit/","shownUrl":"https://ProBolezny.ru/autoimmunnyy-gepatit/","title":"Аутоиммунный гепатит: причины, симптомы и лечение в статье гастроэнтеролога Марченко Н. 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