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В первую очередь страдают поперечно-полосатые мышцы, отвечающие за движения конечностей, а также гладкая мускулатура внутренних органов [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit). \n\n**Особенности**: \n- Хроническое заболевание, у пациентов могут быть периоды обострения и ремиссии [1](https://pmedica.ru/handbook/revmatologiya/dermatomiozit). \n- Чаще всего дерматомиозит встречается у детей до 15 лет и людей зрелого возраста [1](https://pmedica.ru/handbook/revmatologiya/dermatomiozit). \n- В тяжёлых случаях могут быть вовлечены сердце, лёгкие и верхний отдел желудочно-кишечного тракта [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit).\n\n\n\n## Причины\n**Точная причина развития неизвестна** [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche). Некоторые факторы, которые иногда способствуют развитию заболевания: \n* генетическая предрасположенность [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit)[7](https://uteka.ru/articles/bolezni/dermatomiozit/); \n* инфекции (вирусы Эпштейн-Барра, Коксаки, гемолитического стрептококка) [1](https://pmedica.ru/handbook/revmatologiya/dermatomiozit); \n* воздействие ультрафиолетового излучения [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit)[7](https://uteka.ru/articles/bolezni/dermatomiozit/); \n* приём некоторых лекарственных препаратов [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit)[8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche); \n* травмы с повреждением мышц и мягких тканей [7](https://uteka.ru/articles/bolezni/dermatomiozit/). \n\nПримерно в 30% случаев заболевание становится осложнением злокачественных опухолей молочных желёз или внутренних органов — лёгких, поджелудочной, толстой кишки, яичников и других [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche).\n\n## Симптомы\n**Некоторые проявления дерматомиозита**: \n* **Мышечные симптомы**: симптом «рубашки» — трудности при подъёме рук и одевании рубашки из-за слабости плечевых мышц, симптом «лестницы» — сложно подниматься по лестнице из-за слабости мышц бёдер [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit). \n* **Кожные проявления**: папулы Готтрона — красноватые шелушащиеся высыпания на тыльной стороне суставов (чаще всего — пальцы, локти, колени), симптом «шали» — симметричное покраснение и зуд на шее, плечах и зоне декольте, симптом «очков» — отёк и лиловая эритема вокруг глаз [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit). \n* **Вовлечение внутренних органов**: например, развитие интерстициального лёгочного фиброза — плотного рубцевания ткани лёгких, затрудняющего дыхание [4](https://www.katrenstyle.ru/diagnosis_treatment/dermatomiozit).\n\n## Диагностика\n**Для постановки диагноза дерматомиозит** ревматолог может назначить: \n* клинический, биохимический анализы крови, иммунологические исследования [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche); \n* при подозрении на поражения внутренних органов — ЭКГ, УЗИ, КТ, рентгенографию и другие инструментальные исследования [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche); \n* для подтверждения диагноза — биопсию мышц [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche).\n\n## Лечение\n**Лечение дерматомиозита зависит от формы заболевания** [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche): \n* При острой форме необходимо снизить интенсивность симптомов [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche). \n* При хронической — добиться стойкой ремиссии [8](https://ogni.clinic/articles/tpost/4y32o7yfs1-dermatomiozit-simptomi-diagnostika-leche). \n\n**Полностью устранить патологию невозможно**, поэтому в течение всей жизни используют поддерживающую терапию на основе гормонов [2](https://medcentr-Sochi.ru/revmatolog/dermatomiozit.html).","linksData":[{"sourceId":1,"url":"https://pmedica.ru/handbook/revmatologiya/dermatomiozit","shownUrl":"https://pmedica.ru/handbook/revmatologiya/dermatomiozit","title":"Лечение дерматомиозита - Медицинский центр Промедика Белгород","shortUrl":"pmedica.ru","isTranslated":false,"description":"","greenUrl":"pmedica.ru"},{"sourceId":2,"url":"https://medcentr-Sochi.ru/revmatolog/dermatomiozit.html","shownUrl":"https://medcentr-Sochi.ru/revmatolog/dermatomiozit.html","title":"Дерматомиозит: причины, симптомы, диагностика и лечение у врача-ревматолога в МКЦ «Проксима» (г. 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