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Обычно такая почка не отличается от здоровой и выполняет все функции в пределах своего размера [2](https://ProBolezny.ru/gipoplaziya-pochek/). \n\n**Виды гипоплазии почек** [2](https://ProBolezny.ru/gipoplaziya-pochek/): \n* **Односторонняя** — уменьшена только одна почка [2](https://ProBolezny.ru/gipoplaziya-pochek/). \n* **Двусторонняя** — уменьшены оба органа [2](https://ProBolezny.ru/gipoplaziya-pochek/). \n\nПри односторонней гипоплазии часто наблюдается компенсаторное увеличение второй почки [2](https://ProBolezny.ru/gipoplaziya-pochek/).\n\n\n\n## Причины\nГипоплазия почек возникает из-за отклонений внутриутробного развития [1](https://OpenClinics.ru/bolezni/gipoplaziya/pochki/)[6](https://sarmedica.com/blog/gipoplaziya-pochki-u-detej). Некоторые факторы риска: \n* инфекционные заболевания во время беременности (краснуха, токсоплазмоз, грипп) [2](https://ProBolezny.ru/gipoplaziya-pochek/)[6](https://sarmedica.com/blog/gipoplaziya-pochki-u-detej); \n* мутации в генах развития почек (HNF1B, PAX2, PBX1) [2](https://ProBolezny.ru/gipoplaziya-pochek/)[7](https://med-gen.ru/orfapoisk/pochechnaia-gipoplaziia/); \n* хронические заболевания матери (например, сахарный диабет, гипертония) [2](https://ProBolezny.ru/gipoplaziya-pochek/); \n* ионизирующее облучение [2](https://ProBolezny.ru/gipoplaziya-pochek/); \n* маловодие [2](https://ProBolezny.ru/gipoplaziya-pochek/); \n* воздействие высоких температур (например, если беременная долго находится под прямыми солнечными лучами) [2](https://ProBolezny.ru/gipoplaziya-pochek/). \n\nВ 40–60% случаев причину выяснить не удаётся [3](https://www.KrasotaiMedicina.ru/diseases/children/renal-hypoplasia).\n\n## Симптомы\nКлинические проявления гипоплазии почек варьируют в зависимости от степени поражения [5](https://www.mediasphera.ru/issues/arkhiv-patologii/2020/1/1000419552014011042). **При односторонней гипоплазии** и отсутствии критических нарушений мочевыделения болезнь длительное время протекает бессимптомно [3](https://www.KrasotaiMedicina.ru/diseases/children/renal-hypoplasia). **При двустороннем поражении** почечная недостаточность может развиться в раннем возрасте [5](https://www.mediasphera.ru/issues/arkhiv-patologii/2020/1/1000419552014011042). \n\nНекоторые осложнения: хронический пиелонефрит, артериальная гипертензия [5](https://www.mediasphera.ru/issues/arkhiv-patologii/2020/1/1000419552014011042).\n\n## Диагностика\nДиагностика гипоплазии почек основана на данных инструментальной визуализации (УЗИ, КТ, нефросцинтиграфия), лабораторных анализов крови и мочи [3](https://www.KrasotaiMedicina.ru/diseases/children/renal-hypoplasia). \n\n**Диагноз** ставят доношенным детям, если масса почки меньше, чем должна быть в норме, на 0,45% и более [2](https://ProBolezny.ru/gipoplaziya-pochek/).\n\n## Лечение\nЛечение гипоплазии почек зависит от степени поражения [1](https://OpenClinics.ru/bolezni/gipoplaziya/pochki/). **В большинстве случаев** лечение направлено на контроль симптомов и поддержание здоровья почек [8](https://n-d-c.ru/publications/4CCE42E1-5BB4-03DF-53A4-A190C4444F0D/smorshhennaya-pochka/). **В тяжёлых случаях** показана нефрэктомия, трансплантация почки [3](https://www.KrasotaiMedicina.ru/diseases/children/renal-hypoplasia). \n\n**Важно раннее выявление** — без диагностики и наблюдения возможна хроническая почечная недостаточность [1](https://OpenClinics.ru/bolezni/gipoplaziya/pochki/).","linksData":[{"sourceId":1,"url":"https://OpenClinics.ru/bolezni/gipoplaziya/pochki/","shownUrl":"https://OpenClinics.ru/bolezni/gipoplaziya/pochki/","title":"Гипоплазия почки: что это, лечение, симптомы, причины","shortUrl":"OpenClinics.ru","isTranslated":false,"description":"","greenUrl":"OpenClinics.ru"},{"sourceId":2,"url":"https://ProBolezny.ru/gipoplaziya-pochek/","shownUrl":"https://ProBolezny.ru/gipoplaziya-pochek/","title":"Гипоплазия почек: причины, симптомы и лечение в статье уролога Щур А. 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