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Чаще всего речь идёт о **фокально-сегментарном гломерулосклерозе (ФСГС)** — форме гломерулонефрита, для которой характерно склерозирование отдельных сегментов в части клубочков [1](https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS)[4](https://ru.wikipedia.org/wiki/%D0%A4%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE-%D1%81%D0%B5%D0%B3%D0%BC%D0%B5%D0%BD%D1%82%D0%B0%D1%80%D0%BD%D1%8B%D0%B9_%D0%B3%D0%BB%D0%BE%D0%BC%D0%B5%D1%80%D1%83%D0%BB%D0%BE%D1%81%D0%BA%D0%BB%D0%B5%D1%80%D0%BE%D0%B7)[5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz). \n\n**Особенности**: \n- Прогрессирует хронически, может привести к хронической болезни почек [2](https://www.acibademhealthpoint.com/%D0%BF%D1%80%D0%B8%D1%87%D0%B8%D0%BD%D1%8B-%D0%B8-%D0%B4%D0%B8%D0%B0%D0%B3%D0%BD%D0%BE%D1%81%D1%82%D0%B8%D0%BA%D0%B0-%D1%84%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE%D0%B3%D0%BE-%D1%81%D0%B5%D0%B3/). \n- Без лечения состояние может ухудшиться, что может привести к необходимости диализа или трансплантации почек [2](https://www.acibademhealthpoint.com/%D0%BF%D1%80%D0%B8%D1%87%D0%B8%D0%BD%D1%8B-%D0%B8-%D0%B4%D0%B8%D0%B0%D0%B3%D0%BD%D0%BE%D1%81%D1%82%D0%B8%D0%BA%D0%B0-%D1%84%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE%D0%B3%D0%BE-%D1%81%D0%B5%D0%B3/).\n\n\n\n## Причины\nВыделяют **первичный ФСГС** (идиопатический) и **вторичные формы** [1](https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS)[4](https://ru.wikipedia.org/wiki/%D0%A4%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE-%D1%81%D0%B5%D0%B3%D0%BC%D0%B5%D0%BD%D1%82%D0%B0%D1%80%D0%BD%D1%8B%D0%B9_%D0%B3%D0%BB%D0%BE%D0%BC%D0%B5%D1%80%D1%83%D0%BB%D0%BE%D1%81%D0%BA%D0%BB%D0%B5%D1%80%D0%BE%D0%B7)[6](https://cyberleninka.ru/article/n/fokalno-segmentarnyy-glomeruloskleroz-etiopatogeneticheskie-klinicheskie-i-morfologicheskie-osobennosti). Некоторые причины вторичных форм: \n* **Генетические мутации** (аномалии генов ACTN4, NPHS1, CD2AP, TRPC6 и др.) [1](https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS). \n* **Соматические заболевания** (артериальная гипертензия, сахарный диабет, пороки сердца и др.) [1](https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS). \n* **Вирусные инфекции** (ВИЧ-инфекция, заражение парвовирусом В19, вирусами Коксаки) [1](https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS). \n* **Осложнения фармакотерапии** (поражение почек — один из возможных побочных эффектов при продолжительном применении препаратов альфа-интерферона, цитостатиков, иммуносупрессоров) [1](https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS).\n\n## Симптомы\n**Некоторые симптомы ФСГС**: \n* протеинурия (повышенное содержание белка в моче) [5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz); \n* гематурия (наличие крови в моче) [5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz); \n* отёчность ног и лица [5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz); \n* повышенное артериальное давление [5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz); \n* снижение функции почек [5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz). \n\nРанние стадии заболевания могут не вызывать никаких симптомов [3](https://tr-page.yandex.ru/translate?lang=en-ru&url=https%3A%2F%2Fen.wikipedia.org%2Fwiki%2FGlomerulosclerosis).\n\n## Диагностика\n**Для диагностики ФСГС используют**: \n* **Лабораторные анализы** — анализ крови и мочи, оценка уровней белка и креатинина [2](https://www.acibademhealthpoint.com/%D0%BF%D1%80%D0%B8%D1%87%D0%B8%D0%BD%D1%8B-%D0%B8-%D0%B4%D0%B8%D0%B0%D0%B3%D0%BD%D0%BE%D1%81%D1%82%D0%B8%D0%BA%D0%B0-%D1%84%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE%D0%B3%D0%BE-%D1%81%D0%B5%D0%B3/)[5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz). \n* **УЗИ и МРТ почек** [2](https://www.acibademhealthpoint.com/%D0%BF%D1%80%D0%B8%D1%87%D0%B8%D0%BD%D1%8B-%D0%B8-%D0%B4%D0%B8%D0%B0%D0%B3%D0%BD%D0%BE%D1%81%D1%82%D0%B8%D0%BA%D0%B0-%D1%84%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE%D0%B3%D0%BE-%D1%81%D0%B5%D0%B3/). \n* **Биопсию почек** — основной метод, при котором удаляют крошечную часть почки с помощью иглы [2](https://www.acibademhealthpoint.com/%D0%BF%D1%80%D0%B8%D1%87%D0%B8%D0%BD%D1%8B-%D0%B8-%D0%B4%D0%B8%D0%B0%D0%B3%D0%BD%D0%BE%D1%81%D1%82%D0%B8%D0%BA%D0%B0-%D1%84%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE%D0%B3%D0%BE-%D1%81%D0%B5%D0%B3/)[3](https://tr-page.yandex.ru/translate?lang=en-ru&url=https%3A%2F%2Fen.wikipedia.org%2Fwiki%2FGlomerulosclerosis).\n\n## Лечение\n**Лечение ФСГС включает**: \n* **Медикаментозную терапию** — препараты, влияющие на ренин-ангиотензиновую систему (ингибиторы АПФ или блокаторы рецепторов ангиотензина), гиполипидемические препараты, иммуносупрессивную терапию (глюкокортикостероиды, ингибиторы кальциневрина, иммунодепрессанты, моноклональные антитела) [5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz). \n* **Экстракорпоральную гемокоррекцию** — плазмаферез для удаления иммунных комплексов и цитокинов из организма [5](https://yandex.ru/medicine/disease/fokalno-segmentarnyj-glomeruloskleroz). \n\n**Прогноз** зависит от формы заболевания: у значительной части пациентов развивается терминальная стадия почечной недостаточности, требующая заместительной почечной терапии [4](https://ru.wikipedia.org/wiki/%D0%A4%D0%BE%D0%BA%D0%B0%D0%BB%D1%8C%D0%BD%D0%BE-%D1%81%D0%B5%D0%B3%D0%BC%D0%B5%D0%BD%D1%82%D0%B0%D1%80%D0%BD%D1%8B%D0%B9_%D0%B3%D0%BB%D0%BE%D0%BC%D0%B5%D1%80%D1%83%D0%BB%D0%BE%D1%81%D0%BA%D0%BB%D0%B5%D1%80%D0%BE%D0%B7).","linksData":[{"sourceId":1,"url":"https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS","shownUrl":"https://www.KrasotaiMedicina.ru/diseases/zabolevanija_urology/FSGS","title":"Фокально-сегментарный гломерулосклероз - 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