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Названо в честь французского невролога Жиля де ла Туретта, который впервые описал заболевание в 1885 году [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n\nПроявления начинаются в детском или подростковом возрасте, иногда — у молодых людей до 20 лет [1](https://www.rlsnet.ru/library/patient/psixiatriya-i-narkologiya/sindrom-turetta-kak-opredelit-i-lecit-90). Мальчики болеют чаще, но у девочек проблема формируется в более раннем возрасте [1](https://www.rlsnet.ru/library/patient/psixiatriya-i-narkologiya/sindrom-turetta-kak-opredelit-i-lecit-90).\n\n\n\n## Причины\nТочные причины синдрома Туретта до конца не изучены, но учёные выделяют несколько факторов, способствующих развитию заболевания [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/): \n* **Генетическая предрасположенность** — синдром может передаваться по наследству [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). У большинства детей с этим диагнозом есть родственники, страдающие тикозными расстройствами [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n* **Нарушения в работе головного мозга** — считается, что заболевание связано с дисфункцией базальных ганглиев — области мозга, отвечающей за координацию движений и контроль импульсов [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n* **Экологические и перинатальные факторы** — некоторые исследования связывают синдром Туретта с факторами окружающей среды, такими как тяжёлое течение беременности, внутриутробные инфекции, гипоксия плода [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/).\n\n## Симптомы\n**Двигательные тики**: гримасы, почесывания, нахмуривание, кусание губ, непроизвольные прикосновения к предметам или частям тела, пожимания плечами, демонстрация неприличных жестов, прыжки [1](https://www.rlsnet.ru/library/patient/psixiatriya-i-narkologiya/sindrom-turetta-kak-opredelit-i-lecit-90). \n**Звуковые тики**: шипение, кашель, лай, вой, произношение слов и фраз, не имеющих смысловой нагрузки [1](https://www.rlsnet.ru/library/patient/psixiatriya-i-narkologiya/sindrom-turetta-kak-opredelit-i-lecit-90). В некоторых случаях возникает копролалия (выкрикивание нецензурных слов и оскорблений), эхолалия (многократный повтор одних и тех же слов, фраз за собеседником), палилалия (многократное повторение своих собственных слов и фраз) [1](https://www.rlsnet.ru/library/patient/psixiatriya-i-narkologiya/sindrom-turetta-kak-opredelit-i-lecit-90). \n\n**По степени тяжести** проявления симптомов выделяют лёгкую, умеренную, выраженную и тяжёлую степени [1](https://www.rlsnet.ru/library/patient/psixiatriya-i-narkologiya/sindrom-turetta-kak-opredelit-i-lecit-90). Если при лёгкой степени тики практически незаметны и люди могут их контролировать, то при тяжёлой проявления заболевания резкие и ярко выраженные, не поддающиеся контролю [1](https://www.rlsnet.ru/library/patient/psixiatriya-i-narkologiya/sindrom-turetta-kak-opredelit-i-lecit-90).\n\n## Диагностика\n**Диагноз устанавливается на основании клинических проявлений и исключения других неврологических заболеваний** [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). Врач-невролог использует следующие критерии [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/): \n* Наличие моторных и вокальных тиков в течение не менее одного года [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n* Начало заболевания в детском возрасте (до 18 лет) [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n* Переменная интенсивность симптомов [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n* Отсутствие других причин, объясняющих тики (например, травмы мозга, инфекции) [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n\n**Специального лабораторного или генетического теста** для диагностики синдрома Туретта не существует [12](https://gemotest.ru/info/spravochnik/zabolevaniya/sindrom-turetta/).\n\n## Лечение\n**Полного излечения синдрома Туретта не существует**, но существует ряд методов, помогающих контролировать симптомы и улучшить качество жизни пациента [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). Некоторые методы: \n* **Немедикаментозное лечение** — например, когнитивно-поведенческая терапия (КПТ) помогает контролировать тики и снижать тревожность [4](https://alldoctors.moscow/articles/spravochnik-zabolevaniy/sindrom-turetta/). \n* **Медикаментозное лечение** — рекомендуется, когда тики приносят значительный дискомфорт, сопровождаются мышечными болями и травмами [14](https://klinikabudzdorov.ru/diseases-child/sindrom-turetta/). 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